听读43Adrenoleukody



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Thesignalintensityofthecerebellumiswithinnormallimits.Noevidenceofacuteintracranialbleeding,recentinfarct,brainparenchymalhemosiderinstaining,orhydrocephalusisseen.Thebasalcisternsarepatent.Thecerebralsulciandventriclesarenormalinsizeforthepatientsage.Noabnormalextra-axialfluidcollectionisvisible.Flowvoidsofthemajorintracranialvesselsappeargrosslypreserved.

Midlinestructuressuchastheperichiasmalopticnerves/tracts,pituitaryglandandolfactorybulbsappeargrosslynormallyformed.Myelinationpattern(awayfromthesignalchanges)isnormalforage.Nomigrationalanomaly/corticaldysplasiaareapparent.Nomesiotemporalsclerosisisseen.

Themastoidaircellsaremostlyclear,withtraceopacificationontheright.Mildparanasalsinusmucosalthickening.Nogrossorbitalmass.MildbilateralperiopticCSFprominenceisnon-specific.Moderateadenoidalandpalatinetonsillarprominence.

Thisisanothercase,a6-year-oldboypresentedwithprogressivebilateralvisualimpairmentandpoormotorprogressionforhisage,whowasalsodiagnosedwithADL.

Findings:

BilateralsymmetricalcerebralwhitematterhighT2signalchangeinvolvingtheposterior(occipitoparietal)periventricularwhitematter.Sparedfrontallobes.

BilateralsymmetricalhighT2signalchangeinthecorticospinaltracts(pons).

Edgeenhancementoftheextensiveocciptoparietalabnormalities.

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Notes:

1.parenchymal脑实质

2.hemosiderin/?hi:m?usid?rin//?himo?s?d?r?n/n.血黄铁质;含铁血黄素

3.hydrocephalus/?ha?dr?sef(?)l?s//ha?dr?s?f?l?s/n.脑水肿,脑积水

4.cisterns/s?st?n//s?st?n/n.水箱;水池;脑池

5.pituitary/p?tju??t(?)r?//p?tu?t?ri/n.(脑)垂体

6.olfactorybulbs/?lf?kt(?)r?//ɑlf?kt?ri/嗅球

7.myelination/mai?lin?i??n//mai?lin?i??n/n.髓鞘形成

8.mastoid/m?st??d//m?st??d/乳突

9.opacification/?u,p?sifikei??n//?u,p?sifikei??n/n.乳化作用;不透明

10.palatinetonsillar腭扁桃体

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